Fibrosing mediastinitis mimicking sarcoidosis
- PMID: 24405501
- DOI: 10.1111/crj.12107
Fibrosing mediastinitis mimicking sarcoidosis
Abstract
Fibrosing mediastinitis (FM), also called sclerosing mediastinitis or mediastinal fibrosis, is a rare disease characterized by excessive fibrotic reaction in the mediastinum and may compromise the airway, the great vessels and other mediastinal structures, with a morbidity directly related to the location and extent of fibrosis. The cause is not always known but is often the result of a granulomatous disease, most often the histoplasmosis. We report a 43-year-old woman with a history of tuberculosis infection 23 years ago. She attended the pulmonology clinic for cough and dyspnea. Physical examination revealed jugular venous distention at 90°. In computed tomography scan of the chest with contrast (c/c), we observed a mediastinal nodal cast provoking cava compression and obliteration of main and intermediary right lobar bronchus. The pathological examination was FM.
Keywords: IgG4-related disease; fibrosing mediastinitis; sarcoidosis.
© 2014 John Wiley & Sons Ltd.
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