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Review
. 2014 Apr;33(2):109-13.
doi: 10.3109/15513815.2013.878009. Epub 2014 Jan 28.

Rapidly fatal "congenital lung dysplasia": a case report and review of the literature

Massimiliano Don  1 , Maria Orsaria, Eva Da Dalt, Carmela Tringali, Bruno Sacher
Affiliations
Review

Rapidly fatal "congenital lung dysplasia": a case report and review of the literature

Massimiliano Don et al. Fetal Pediatr Pathol. 2014 Apr.

Abstract

Acinar dysplasia congenital alveolar dysplasia and alveolar capillary dysplasia with misalignment of pulmonary veins belong to the diffuse developmental disorders (congenital lung dysplasia), very rare fatal disorders of infancy that occur early in lung development. A case of quickly fatal congenital lung dysplasia in a full-term infant is presented and underlines the necessity to suspect this disease in a newborn suffering from severe and refractory respiratory distress.

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