Epstein-barr virus-induced hemophagocytic lymphohistiocytosis
- PMID: 24505517
- PMCID: PMC3913132
Epstein-barr virus-induced hemophagocytic lymphohistiocytosis
Abstract
Hemophagocytic lymphohistiocytosis (HLH) is one of the complications of Epstein-Barr virus (EBV) infection. Although the patients who have developed HLH following EBV have normal immune system, there are a few patients with EBV-induced immune deficiency who develop HLH as well. Here, we describe the case of a 10-year-old girl with neurological complications caused by EBV-induced HLH. The patient received rituximab, leading to weakening inflammation associated with EBV infection and suppression of disease through quick treatment.
Keywords: Epstein - Barr virus; Etanercept; Hemophagocytic lymphohistiocytosis; Infectious mononucleosis; Systemic inflammatory response syndrome; X-Linked lymphoproliferative disease.
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