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Case Reports
. 2013 Sep;17(3):478.
doi: 10.4103/0973-029X.125226.

Primary fibrosarcoma of maxilla in an 8-year-old child: A rare entity

Niharika Swain  1 , Shwetha V Kumar  2 , Richa Dhariwal  2 , Samapika Routray  3
Affiliations
Case Reports

Primary fibrosarcoma of maxilla in an 8-year-old child: A rare entity

Niharika Swain et al. J Oral Maxillofac Pathol. 2013 Sep.

Abstract

Fibrosarcoma (FS) is a malignant mesenchymal neoplasm of the fibroblasts that is uncommon in the head and neck and constitutes less than 1% of malignancies and approximately 6% of the soft tissue sarcomas. FSs rarely occur before the third decade except infantile type. This condition primarily affects long bones, and its occurrence in the cranium is rare (15%), with the mandible being the most commonly involved cranial site. Here a case of primary FS in anterior maxilla of an 8-year-old male child is reported. This article is presented to document the rarity of FSs in the jaws of children with review of literature.

Keywords: Bone; child; fibrosarcoma; maxilla.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
A large swelling on anterior maxilla extending from 55 to 65
Figure 2
Figure 2
Orthopantomograph revealed a purely osteolytic lesion in the anterior maxilla
Figure 3
Figure 3
Highly cellular stroma arranged in interlacing fascicles showing herringbone pattern (H&E stain, ×400)
Figure 4
Figure 4
Neoplastic spindle-shaped cells showing mitotic figures (H&E stain,×400)
Figure 5
Figure 5
Tumor cells showing intense immunoreactivity for vimentin (IHC stain, ×200)
See this image and copyright information in PMC

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