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. 2014 Jan;11(1-2):26-8.

Would You Recognize Fahr's Disease if You Saw It?

Dharmendra Goyal  1 , Mashal Khan  1 , Bushra Qureshi  1 , Catherine Mier  1 , Steven Lippmann  1
Affiliations

Would You Recognize Fahr's Disease if You Saw It?

Dharmendra Goyal et al. Innov Clin Neurosci. 2014 Jan.

Abstract

Idiopathic basal ganglia calcification or Fahr's disease is a neurological condition with a prominent movement disorder. Diagnostically, brain imaging with computerized tomographic scanning reveals bilateral brain calcifications, usually of the basal ganglia. A positive family history is very common, along with a generational anticipatory effect, thus familial basal ganglia calcification is an alternative name. Cognitive deficits and psychiatric symptoms are often present. This progressive disease has no cure, but symptomatic treatment may be beneficial.

Keywords: CT scan; Fahr’s disease; cerebral calcification; cognitive deficit; dementia; idiopathic basal ganglia calcification; movement disorder.

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Figures

FIGURES 1 and 2.
FIGURES 1 and 2.
Computerized tomographic scans of the head in 2010 (Figure 1) and 2013 (Figure 2) reveal coarse bilateral, symmetrical calcifications in the basal ganglia, with progression in 2013.
FIGURES 1 and 2.
FIGURES 1 and 2.
Computerized tomographic scans of the head in 2010 (Figure 1) and 2013 (Figure 2) reveal coarse bilateral, symmetrical calcifications in the basal ganglia, with progression in 2013.
See this image and copyright information in PMC

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