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. 2014 Jan;18(1):113-5.
doi: 10.4103/2230-8210.126589.

An unusual presentation of Hashimoto's encephalopathy

Rajeev Philip  1 , Sanjay Saran  1 , Manish Gutch  1 , Keshavkumar Gupta  1
Affiliations

An unusual presentation of Hashimoto's encephalopathy

Rajeev Philip et al. Indian J Endocrinol Metab. 2014 Jan.

Abstract

Hashimoto's encephalopathy (HE) is a rare steroid-responsive encephalopathy syndrome, which can have highly variable neuropsychiatric manifestations and can go unrecognized for a long time. HE is a diagnosis of exclusion and should be kept in mind when evaluating a patient with a cognitive dysfunction and high titers of anti-thyroid antibodies as it responds dramatically to steroids. Steroid responsive myoclonus can be a presentation of HE.

Keywords: Anti-thyroid antibodies; Hashimoto encephalopathy; autoimmune thyroid disease; hypothyroidism; steroid responsive encephalopathy.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Electroencephalogram showing diffuse slow wave activity
Figure 2
Figure 2
Magnetic resonance images showing pituitary hyperplasia
Figure 3
Figure 3
Magnetic resonance images showing non-specific White matter changes
See this image and copyright information in PMC

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