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Case Reports
. 2014 Apr;4(2):48-50.
doi: 10.4103/2231-0770.130347.

A concurrent episode of two neoplasms in a toddler-age child

Muaz A Alrazzak  1 , Jenny Zablahalabi  2 , Baraa Alrazzak  3 , Guillermo De Angulo  2
Affiliations
Case Reports

A concurrent episode of two neoplasms in a toddler-age child

Muaz A Alrazzak et al. Avicenna J Med. 2014 Apr.

Abstract

Childhood neoplasms are relatively rare and represent only about 1- 2% of the total incidence of neoplasms in United States. Concurrent episode of childhood cancer is uncommon and usually related to a cancer genetic syndrome. Li Fraumeni Syndrome refers to an autosomal dominant condition that is manifested by the development of certain cancers in early childhood and an increased lifetime risk for developing multiple primary cancers including sarcoma, breast cancer, leukemia, bone cancer, and others. We report a case of a 21-month-old girl who was found to have orbital embryonal rhabdomyosarcoma and adrenocortical tumor concurrently.

Keywords: Adrenocortical tumor; Li Fraumeni syndrome; orbital rhabdomyosarcoma.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
(a) The orbital Computed Tomography scan showing left retro-orbital mass. (b) Left eye proptosis at presentation (verbal permission was taken from the guardians)
Figure 2
Figure 2
Positron Emission Tomography scan revealing a PET avid mass in the left suprarenal area.
See this image and copyright information in PMC

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