A rare case of underlying pulmonary sequestration in a patient with recently diagnosed medium and large vessel vasculitis

Abstract

Vasculitis of medium- and large-sized arteries is an inflammatory and stenotic disease characterized by a strong predilection for the aortic arch and its branches. It presents with symptoms and signs as per the vessels and organs involved. Pulmonary sequestration is a rare abnormality characterized by a mass of nonfunctioning lung tissue that receives its vascular supply from a systemic artery and is separated from the normal tracheobronchial tree. The following is a rare case report showing the presence of pulmonary sequestration in a patient with recently diagnosed hypertension and intestinal angina due to medium and large vessel vasculitis.

Keywords: Intralobar lung sequestration; lung sequestration; vasculitis.

Figure 1

Axial computed tomography sections of the thorax showing heterogeneous segment (black arrow) in the medial basal segment of the left lung deriving its arterial supply from the descending aorta (white arrow)

Figure 2

Saggital contrast enhanced computed tomography image showing thickened wall of the descending aorta with narrowing of the caliber (large arrow). Volume-rendered angiographic images shows narrowing of the superior mesenteric artery (small arrow) with stenosis of bilateral renal arteries involving the ostia and proximal segments (double arrows) with post-stenoticdilatation. The arterial branch to the sequestered lung segment from the thoracic aorta is well seen in the central angiographic image