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Case Reports
. 2014 Apr 7;4(2):e15460.
doi: 10.5812/aapm.15460. eCollection 2014 May.

Laparoscopic cortical sparing adrenalectomy for pediatric bilateral pheochromocytoma: anesthetic management

Affiliations
Case Reports

Laparoscopic cortical sparing adrenalectomy for pediatric bilateral pheochromocytoma: anesthetic management

Geetha Chamanhalli Rajappa et al. Anesth Pain Med. .

Abstract

Introduction: Pheochromocytoma is a catecholamine-secreting tumor, which is seen rarely in children. These tumors predominantly secrete norepinephrine and epinephrine. They might be familial and associated with hereditary tumors such as Von Hippel-Lindau syndrome and multiple endocrine neoplasia type II.

Case presentation: The child might present with a spectrum of clinical manifestation including hypertension, headache, visual disturbances, and behavioral problems. A meticulous preoperative preparation is essential for a stable intraoperative and postoperative outcome.

Conclusions: We described successful perioperative management of a child who underwent bilateral laparoscopic cortical sparing adrenalectomy and a repeated surgery for the residual tumor removal.

Keywords: Adrenalectomy; Anesthetics; Laparoscopy; Pediatrics; Pheochromocytoma.

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Figures

Figure 1.
Figure 1.. A: CT Scan of Abdomen Revealed Bilateral Pheochromocytoma, B: [123] I-Labelled MIBG Scan Showing Inconclusive Findings, C and D: PET Scan Revealed Metabolically Active Enhancing Nodule in the Right Suprarenal Region

References

    1. Havekes B, Romijn JA, Eisenhofer G, Adams K, Pacak K. Update on pediatric pheochromocytoma. Pediatr Nephrol. 2009;24(5):943–50. doi: 10.1007/s00467-008-0888-9. - DOI - PubMed
    1. Waguespack SG, Rich T, Grubbs E, Ying AK, Perrier ND, Ayala-Ramirez M, et al. A current review of the etiology, diagnosis, and treatment of pediatric pheochromocytoma and paraganglioma. J Clin Endocrinol Metab. 2010;95(5):2023–37. doi: 10.1210/jc.2009-2830. - DOI - PubMed
    1. Chen H, Sippel RS, O'Dorisio MS, Vinik AI, Lloyd RV, Pacak K, et al. The North American Neuroendocrine Tumor Society consensus guideline for the diagnosis and management of neuroendocrine tumors: pheochromocytoma, paraganglioma, and medullary thyroid cancer. Pancreas. 2010;39(6):775–83. doi: 10.1097/MPA.0b013e3181ebb4f0. - DOI - PMC - PubMed
    1. Timmers HJ, Kozupa A, Chen CC, Carrasquillo JA, Ling A, Eisenhofer G, et al. Superiority of fluorodeoxyglucose positron emission tomography to other functional imaging techniques in the evaluation of metastatic SDHB-associated pheochromocytoma and paraganglioma. J Clin Oncol. 2007;25(16):2262–9. doi: 10.1200/JCO.2006.09.6297. - DOI - PubMed
    1. Pacak K. Preoperative management of the pheochromocytoma patient. J Clin Endocrinol Metab. 2007;92(11):4069–79. doi: 10.1210/jc.2007-1720. - DOI - PubMed

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