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. 2014 May 15;113(10):1735-9.
doi: 10.1016/j.amjcard.2014.03.001. Epub 2014 Mar 14.

Arrhythmogenic right ventricular dysplasia back in force

Guy Fontaine  1 , Huei-Sheng Vincent Chen  2
Affiliations

Arrhythmogenic right ventricular dysplasia back in force

Guy Fontaine et al. Am J Cardiol. .
No abstract available

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Figures

Figure 1
Figure 1
This sanguine by Leonardo da Vinci is impressive by the enlargement and the thinness of RV.
Figure 2
Figure 2
Score of fat in the RV from 82 patients aged 15 to 75 years old, who died from a noncardiac cause in a general hospital of Paris (Dr. Fabrice Fontaliran study). Quiescent right ventricular dysplasia observed in 4% of this study showed the same amount of fat than the score IV plus interstitial fibrosis. Fat dissociation syndrome has occasionally been called less precisely as coradiposum or adipositas cordis because cover of pure fat on epicardium remains within normal limits. However, rupture during acute myocardial infarction is more common in the fatty heart than in the nonfatty heart (Roberts WC and Roberts JD36).
Figure 3
Figure 3
Irreversible RV failure after heart transplantation. RV myocardium mostly replaced by fat without fibrosis. (20 Sirius Red staining, courtesy of Pr Paul Fornes, Paris).
See this image and copyright information in PMC

Comment in

References

    1. Fontaine G, Guiraudon G, Frank R, Vedel J, Grosgogeat Y, Cabrol C, Facquet J. Stimulation studies and epicardial mapping in ventricular tachycardia: study of mechanisms and selection for surgery. In: Kulbertus HE, editor. Reentrant Arrhythmias. Lancaster: MTP Pub; 1977. p. 334e350.
    1. Fontaine G, Guiraudon G, Frank R. Intramyocardial conduction defects in patients prone to ventricular tachycardia. I- The postexcitation syndrome in sinus rhythm p39e55, II- A dynamic study of the postexcitation syndrome p56–66, III- The Post-Excitation Syndrome During Ventricular Tachycardia p67–79. In: Sandoe E, Julian DG, Bell JW, editors. Management of Ventricular Tachycardia. Role of Mexiletine. Excerpta Medica Pub; Amsterdam: 1978.
    1. Marcus FI, Fontaine G, Guiraudon G, Frank R, Laurenceau JL, Malergue MC, Grosgogeat Y. Right ventricular dysplasia: a report of 24 cases. Circulation. 1982;65:384, e399. - PubMed
    1. Uhl HS. A previously undescribed congenital malformation of the heart: almost total absence of the myocardium of the right ventricle. Bull John Hopkins Hosp. 1952;91:197, e205. - PubMed
    1. James TN, Nichols MM, Sapire DW, DiPatre PL, Lopez SM. Complete heart block and fatal right ventricular failure in an infant. Circulation. 1996;93:1588, e1600. - PubMed

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