Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2014 May;59(3):316.
doi: 10.4103/0019-5154.131459.

Adult-onset unilateral disabling pansclerotic morphea

Adarshlata Singh  1 , Kritika Singhal  1 , Sanjiv Choudhary  1 , Shazia Bisati  1 , Mallika Arora  1
Affiliations

Adult-onset unilateral disabling pansclerotic morphea

Adarshlata Singh et al. Indian J Dermatol. 2014 May.

Abstract

Disabling pansclerotic morphea (DPM) is a rare, severe, and mutilating form of morphea, involving the dermis, subcutaneous tissue, fat, muscle, and even bone. It is usually seen before the age of 14 years, with the patient complaining of arthralgia and stiffness at the time of onset. We report a case of unilateral adult-onset DPM with sparing of the face. Within a few months of onset, painful contracture deformities of the hand, elbow, and shoulder joints developed, impairing the patient's normal daily activities. We are reporting this case because of the unusual presentation: DPM in an adult, with history of trauma in childhood and rapid onset of complications, is rare.

Keywords: Adult; disabling pansclerotic morphea; methotrexate; systemic corticosteroids.

PubMed Disclaimer

Conflict of interest statement

Conflict of Interest: Nil.

Figures

Figure 1
Figure 1
Binding down of skin
Figure 2
Figure 2
Pretreatment contracture on the left side
Figure 3
Figure 3
X-ray of affected limb showing osteoporosis
Figure 4
Figure 4
Post-treatment improvement at the affected site
See this image and copyright information in PMC

Similar articles

See all similar articles

References

    1. Sawhney MP. Facial hemiatrophy of Romberg and Parry. Indian J Dermatol Venereol Leprol. 1991;57:41–2.
    1. Hickman JW, Shiels WS. Progressive facial hemiatrophy. Arch intern Med. 1964;113:716–7. - PubMed
    1. Padmavathy L, Rao LL. Unilateral linear pansclerotic morphea affecting face and limbs. Indian J Dermatol Venereol Leprol. 2005;71:192–4. - PubMed
    1. Rowell NR. Acral pansclerotic morphoea with intractable pain. In: Burgdorf WH, Katz SI, editors. Clinical dermatology: The CMO case collection/world congress of dermatology. Berlin: Scheltauer; 1987. pp. 178–80.
    1. Maragh SH, Davis MD, Bruce AJ, Nelson AM. Disabling pansclerotic morphea: Clinical presentation in two adults. J Am Acad Dermatol. 2005;53:S115–9. - PubMed

LinkOut - more resources