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. 2014 May;59(3):316.
doi: 10.4103/0019-5154.131459.

Adult-onset unilateral disabling pansclerotic morphea

Adarshlata Singh  1 , Kritika Singhal  1 , Sanjiv Choudhary  1 , Shazia Bisati  1 , Mallika Arora  1
Affiliations

Adult-onset unilateral disabling pansclerotic morphea

Adarshlata Singh et al. Indian J Dermatol. 2014 May.

Abstract

Disabling pansclerotic morphea (DPM) is a rare, severe, and mutilating form of morphea, involving the dermis, subcutaneous tissue, fat, muscle, and even bone. It is usually seen before the age of 14 years, with the patient complaining of arthralgia and stiffness at the time of onset. We report a case of unilateral adult-onset DPM with sparing of the face. Within a few months of onset, painful contracture deformities of the hand, elbow, and shoulder joints developed, impairing the patient's normal daily activities. We are reporting this case because of the unusual presentation: DPM in an adult, with history of trauma in childhood and rapid onset of complications, is rare.

Keywords: Adult; disabling pansclerotic morphea; methotrexate; systemic corticosteroids.

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Conflict of interest statement

Conflict of Interest: Nil.

Figures

Figure 1
Figure 1
Binding down of skin
Figure 2
Figure 2
Pretreatment contracture on the left side
Figure 3
Figure 3
X-ray of affected limb showing osteoporosis
Figure 4
Figure 4
Post-treatment improvement at the affected site
See this image and copyright information in PMC

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