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Case Reports
. 2014 Mar-Apr;34(2):167-70.
doi: 10.5144/0256-4947.2014.167.

Cochlear implant for bilateral profound sensorineural hearing loss in an adolescent with sickle cell anemia

Fida Abdulaziz Almuhawas, Abdulrahman Abdullah Hagr  1
Affiliations
Case Reports

Cochlear implant for bilateral profound sensorineural hearing loss in an adolescent with sickle cell anemia

Fida Abdulaziz Almuhawas et al. Ann Saudi Med. 2014 Mar-Apr.

Abstract

We present the first-published cochlear implant in an adolescent with sickle cell anemia (SCA) and bilateral profound sensorineural hearing loss (SNHL). A 15-year-old Saudi girl, previously diagnosed with SCA, developed gradual bilateral permanent profound SNHL over 18 months and underwent a successful cochlear implantation. SNHL associated with sickle cell crises is a well-known phenomenon. Regular hearing assessments are recommended for sickle cell patients, and early referrals for cochlear implantations are advocated for those with permanent profound SNHL.

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Figures

Figure 1
Figure 1
Pure-tone audiograms showing bilateral profound SNHL.
Figure 2
Figure 2
Octoacoustic emissions were absent in both ears.
Figure 3
Figure 3
CT scan bone window showing an axial cut of the temporal bones without contrast through the level of the promontory, revealing normal anatomy.
See this image and copyright information in PMC

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