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Case Reports
. 2014 Mar-Apr;34(2):167-70.
doi: 10.5144/0256-4947.2014.167.

Cochlear implant for bilateral profound sensorineural hearing loss in an adolescent with sickle cell anemia

Fida Abdulaziz Almuhawas, Abdulrahman Abdullah Hagr  1
Affiliations
Case Reports

Cochlear implant for bilateral profound sensorineural hearing loss in an adolescent with sickle cell anemia

Fida Abdulaziz Almuhawas et al. Ann Saudi Med. 2014 Mar-Apr.

Abstract

We present the first-published cochlear implant in an adolescent with sickle cell anemia (SCA) and bilateral profound sensorineural hearing loss (SNHL). A 15-year-old Saudi girl, previously diagnosed with SCA, developed gradual bilateral permanent profound SNHL over 18 months and underwent a successful cochlear implantation. SNHL associated with sickle cell crises is a well-known phenomenon. Regular hearing assessments are recommended for sickle cell patients, and early referrals for cochlear implantations are advocated for those with permanent profound SNHL.

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Figures

Figure 1
Figure 1
Pure-tone audiograms showing bilateral profound SNHL.
Figure 2
Figure 2
Octoacoustic emissions were absent in both ears.
Figure 3
Figure 3
CT scan bone window showing an axial cut of the temporal bones without contrast through the level of the promontory, revealing normal anatomy.
See this image and copyright information in PMC

References

    1. Samperi P, Bertuna G, Rossi G, Poli G, Serra A. Sensorineural hearing loss in sickle cell disease patients in Sicily. Minerva Pediatr. 2005;57:285–288. - PubMed
    1. Mgbor N, Emodi I. Sensorineural hearing loss in Nigerian children with sickle cell disease. Int J Pediatr Otorhinolaryngol. 2004;68:1413–1416. - PubMed
    1. Ajulo SO, Osiname AI, Myatt HM. Sensorineural hearing loss in sickle cell anaemia--a United Kingdom study. J Laryngol Otol. 1993;107:790–794. - PubMed
    1. Jovanovic-Bateman L, Hedreville R. Sensorineural hearing loss with brainstem auditory evoked responses changes in homozygote and heterozygote sickle cell patients in Guadeloupe (France) J Laryngol Otol. 2006;120:627–630. - PubMed
    1. Whitehead RE, MacDonald CB, Melhem ER, Mc-Mahon L. Spontaneous labyrinthine hemorrhage in sickle cell disease. AJNR Am J Neuroradiol. 1998;19:1437–1440. - PMC - PubMed

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