Complete congenital foetal heart block: a case report
- PMID: 25009724
- PMCID: PMC4086001
Complete congenital foetal heart block: a case report
Abstract
Congenital heart block (CHB) is the most severe manifestation of neonatal lupus which can develop into a lethal atrioventricular (AV) block. Complete congenital foetal heart block related to maternal anti-Ro/SSA autoanti-bodies typically develops between 20 and 24 weeks of gestation. CHB with a structurally normal heart is frequently associated with maternal autoantibodies to Ro/SSA and La/SSB. We are presenting a case of foetal complete CHB with high maternal Ro/SSA and La/SSB titre with favourable outcome.
Keywords: Congenital heart block; Dexamethasone; La/SSB; Ro/SSA; SLE.
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