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. 2014 Jul;59(4):421.
doi: 10.4103/0019-5154.135530.

Becker's Nevus Syndrome

Sathyanarayana B Dasegowda  1 , Gb Basavaraj  1 , Kc Nischal  1 , Mr Swaroop  1 , Np Umashankar  1 , Suchetha S Swamy  1
Affiliations

Becker's Nevus Syndrome

Sathyanarayana B Dasegowda et al. Indian J Dermatol. 2014 Jul.

Abstract

Becker's nevus is a cutaneous hamartoma characterized by circumscribed hyperpigmentation with hypertrichosis. Becker's nevus syndrome is an association of Becker's nevus with unilateral breast hypoplasia and muscle, skin, and/or skeletal abnormalities. We here report a case of a 15 year-old female who presented with bilateral Becker's nevus over her groins, thighs, vulva, and in front of the neck from the age of 5 years. She had associated mental retardation, delayed development of mile stones, delayed puberty, dwarfism, depressed nasal bridge, long slender digits, crowding of lateral toes, valgus deformity of first metatarsophalangeal joint, mitral valve prolapse, muddy conjunctiva with hypertrophic and hyperpigmented caruncle of both eyes, ichthyosis, brownish hair, and absence of axillary and pubic hair. On histopathological examination collagen hamartoma underneath the Becker's nevus was found.

Keywords: Becker's nevus; Becker's nevus syndrome; collagen hamartoma.

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Conflict of interest statement

Conflict of Interest: Nil.

Figures

Figure 1
Figure 1
Hyperpigmented, hyperkeratotic, indurated plaque over groins, vulva, and anteromedial aspect of the thighs
Figure 2
Figure 2
Hyperpigmented plaque over the anterior aspect of the neck
Figure 3
Figure 3
Syndactyly of left 4th and 5th toes with left great toe halux valgus deformity
Figure 4
Figure 4
Hyperkeratosis, acanthosis, elongated rete ridges, increased pigmentation of basal keratinocytes from a hyperpigmented, and hyperkeratotic plaque over groin area (H and E, ×100)
Figure 5
Figure 5
Increased dermal collagen proliferation observed on special stain (Van Gieson, × 100)
See this image and copyright information in PMC

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