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Case Reports
. 2014 Sep;30(3):204-7.
doi: 10.1007/s12288-012-0210-7. Epub 2012 Nov 22.

Hemophagocytic lymphohistiocytosis

A M V R Narendra  1 , G Varun Kumar  1 , A Krishna Prasad  1 , M Shetty  1 , Megha S Uppin  2 , V R Srinivasan  1
Affiliations
Case Reports

Hemophagocytic lymphohistiocytosis

A M V R Narendra et al. Indian J Hematol Blood Transfus. 2014 Sep.

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is an immune disorder characterized by uncontrolled inflammation due to defective immune response. It may be familial or acquired, but both share a common feature of threatening the life of a patient and may lead to death unless treated by appropriate treatment. Here in we report a case of adult HLH.

Keywords: HLH; NK cell dysfunction; PUO.

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Figures

Fig. 1
Fig. 1
Bone marrow aspirate smears showing prominence of histiocyte with phagocytosis of hematopoietic precursors. GiemsaX400
Fig. 2
Fig. 2
The histiocyte in trephine biopsy showing phagocytosis. H&EX400
See this image and copyright information in PMC

References

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