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Case Reports
. 2013 Apr;20(2):80-2.
doi: 10.5214/ans.0972.7531.200211.

Primary spinal primitive neuroectodermal tumour - a case report

Sundar Venkataraman  1 , Chelladurai Pandian  1 , Suresh A Kumar  1
Affiliations
Case Reports

Primary spinal primitive neuroectodermal tumour - a case report

Sundar Venkataraman et al. Ann Neurosci. 2013 Apr.

Abstract

Primitive neuroectodermal tumours (PNET) are aggressive childhood malignancies and offer a significant challenge to treatment. A two years old female child presented with weakness both lower limbs. Preoperative MRI of the spine and paravertebral regionIso - hyper intense posterior placed extradural lesion, non contrast enhancing from D11-L2 levels with cord compression D9 to L3 laminectomy done. Granulation tissue found from D11 to L2. with cord compression. The granulation tissue removed in toto. The pathological findings were consistent with PNET. Post operative neurological improvement was minimal. Cranial screening ruled out any intracranialtumour. Hence a diagnosis of primary spinal PNET was made. A review of the literature shows that only 19 cases of primary intraspinal PNETs have been reported to date and the present case extradural in location. Primary intraspinal PNETs are rare tumors and carry a poor prognosis.

Keywords: Primitive neuroectodermal tumor (PNET); Spinal cord.

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Figures

Fig. 1:
Fig. 1:
MRI of the spine which revealing an iso – hyper intense posterior placed extradural lesion , non contrast enhancing from D11-L2 levels with cord compression.
See this image and copyright information in PMC

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