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Case Reports
. 2014 Oct;26(77):263-6.

First branchial cleft fistula associated with external auditory canal stenosis and middle ear cholesteatoma

Shahin Abdollahi Fakhim  1 , Masoud Naderpoor  2 , Mehrnoosh Mousaviagdas  1
Affiliations
Case Reports

First branchial cleft fistula associated with external auditory canal stenosis and middle ear cholesteatoma

Shahin Abdollahi Fakhim et al. Iran J Otorhinolaryngol. 2014 Oct.

Abstract

Introduction: First branchial cleft anomalies manifest with duplication of the external auditory canal.

Case report: This report features a rare case of microtia and congenital middle ear and canal cholesteatoma with first branchial fistula. External auditory canal stenosis was complicated by middle ear and external canal cholesteatoma, but branchial fistula, opening in the zygomatic root and a sinus in the helical root, may explain this feature. A canal wall down mastoidectomy with canaloplasty and wide meatoplasty was performed. The branchial cleft was excised through parotidectomy and facial nerve dissection.

Conclusion: It should be considered that canal stenosis in such cases can induce cholesteatoma formation in the auditory canal and middle ear.

Keywords: Canal stenosis; Cholesteatoma.; First branchial cleft; fistula.

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Figures

Fig 1
Fig 1
First branchial cleft fistula opening in the middle ear and mastoid cholesteatoma
Fig. 2
Fig. 2
Computed tomography (CT) scan from first branchial cleft fistula opening in the middle ear showing automastoidectomy and the appearance of soft tissue in the middle ear and mastoid
Fig 3
Fig 3
First branchial fistula and its tract to the zygomatic root shown via fistulography
Fig. 4
Fig. 4
Intraoperative view of parotidectomy and fistula resection in the case of branchial fistula
See this image and copyright information in PMC

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