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Case Reports
. 2015 Mar;48(3):e73-5.
doi: 10.1016/j.jemermed.2014.09.064. Epub 2014 Dec 8.

Herlyn-Werner-Wunderlich syndrome: a very rare urogenital anomaly in a teenage girl

Leyla Karaca  1 , Berhan Pirimoglu  1 , Ummugulsum Bayraktutan  1 , Hayri Ogul  1 , Akgun Oral  2 , Mecit Kantarci  1
Affiliations
Case Reports

Herlyn-Werner-Wunderlich syndrome: a very rare urogenital anomaly in a teenage girl

Leyla Karaca et al. J Emerg Med. 2015 Mar.

Abstract

Background: Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon variant of Müllerian duct anomalies, consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in a post-pubertal adolescent or adult woman in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina.

Case report: We report the case of a 13-year-old girl who presented to the emergency radiology department with sudden onset of severe pain at the right lower quadrant of the abdomen; imaging confirmed the diagnosis of HWW syndrome. WHY SHOULD AN EMERGENCY PHYSICIAN BE AWARE OF THIS?: When unilateral renal agenesis and uterus didelphys coexist, the first thing that the physician should remember is to confirm or refute the presence of a blind vagina for diagnosis of HWW syndrome.

Keywords: Herlyn Werner Wunderlich syndrome; Müllerian duct anomalies; hematocolpos; renal agenesis.

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