[Klippel-Trenaunay-Weber syndrome with papillary cystadenoma of the epididymis: a case report]

Abstract

A case of Klippel-Trenaunay-Weber syndrome with papillary cystadenoma of the right epididymis is reported. A 7-year-old boy visited our clinic on October 19, 1985 with a tender right intra-scrotal mass (35 X 15 m) and pyuria. In spite of the initial treatment with antibiotics, the tumor grew larger in December, 1987. The patient underwent right orchiectomy on December 23, 1987. Macroscopically, the specimen measured 40 X 23 X 20 mm and weighed 17 g. Histological examinations demonstrated that the tumor was papillary cystadenoma of the right epididymis. The patient lacked the signs of von Hippel-Lindau disease since there were no abnormal findings on brain and abdominal computer tomographic scan, and retinae were normal on fundoscopic examinations.