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Case Reports
. 2015 Jan 27:2015:bcr2013202509.
doi: 10.1136/bcr-2013-202509.

Association of pulmonary silicosis and systemic sclerosis

Kaouther Ben Abdelghani  1 , Alia Fazaa  1 , Leila Souabni  1 , Leith Zakraoui  1
Affiliations
Case Reports

Association of pulmonary silicosis and systemic sclerosis

Kaouther Ben Abdelghani et al. BMJ Case Rep. .

Abstract

The Erasmus syndrome describes the association of generalised systemic sclerosis following exposure to silica with or without silicosis. This is a case report on a male patient presenting with this syndrome. Radiological changes of silicosis have preceded the diagnosis of systemic sclerosis by 6 years and occupational exposure has been stopped. The clinical features did not differ from systemic sclerosis in general. The evolution was marked by a progression of skin lesions whereas pulmonary lesion remained stable.

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Figures

Figure 1
Figure 1
Erosion of the ulnar styloid with metacarpal pinching.
Figure 2
Figure 2
Interstitial syndrome with a para-hilar and left pulmonary base reticulo-nodular appearance.
Figure 3
Figure 3
Chest CT scan: parenchymal retractile condensation of the left basal pyramid with bronchiectasis and hyperdensity ranges in frosted glass.
See this image and copyright information in PMC

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References

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