Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2015 Jan;3(1):19-23.
doi: 10.1002/ccr3.137. Epub 2014 Sep 15.

A successful early gore-tex reconstruction of an abdominal wall defect in a neonate with Cantrell pentalogy: a case report and literature review

Affiliations
Case Reports

A successful early gore-tex reconstruction of an abdominal wall defect in a neonate with Cantrell pentalogy: a case report and literature review

Dalibor Divkovic et al. Clin Case Rep. 2015 Jan.

Abstract

A surgical technique, materials used for abdominal wall reconstruction, and postoperative care are important for patient outcomes. We report the first case of neonate with Cantrell's pentalogy surviving early reconstruction of abdominal, diaphragmal and pericardial defects. Several recent investigations suggest that intraabdominal pressure monitoring may improve outcomes in this patient category.

Keywords: Congenital abnormalities; herniorrhaphy; intensive care; intraabdominal hypertension; mesh repair; monitoring; omphalocele; pentalogy of Cantrell.

PubMed Disclaimer

Figures

Figure 1
Figure 1
(A) A major omphalocele with liver in the central position. (B) A defect of the ventral part of diaphragm, aplastic lower sternum, defective hypoplastic pericardium, and caudal displacement of heart. (C) A reconstruction of diaphragm with direct stitches after mobilizing the posterior leaf. (D) A polytetrafluoroethylene patch used for the staged abdominal wall reconstruction with pericardial drain and umbilical vein catheter in situ. (E) A scar plate formation below the mesh. (F) A boy at the age of 4. Rectus muscles seem to be retracted with no signs of reherniation.

References

    1. Cantrell JR, Haller JA. Ravitch MM. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium and heart. Surg. Gynecol. Obstet. 1958;107:602–614. - PubMed
    1. Vazquez-Jimenez JF, Muehler EG, Daebritz S, Keutel J, Nishigaki K, Huegel W, et al. Cantrell's syndrome: a challenge to the surgeon. Ann. Thorac. Surg. 1998;65:1178–1185. - PubMed
    1. Engum SA. Embryology, sternal clefts, ectopia cordis, and Cantrell's pentalogy. Semin. Pediatr. Surg. 2008;17:154–160. - PubMed
    1. Wheeler DS. St Louis JD. Pentalogy of Cantrell associated with hypoplastic left heart syndrome. Pediatr. Cardiol. 2007;28:311–313. - PubMed
    1. Saxena AK. van Tuil C. Delayed three-stage closure of giant omphalocele using pericard patch. Hernia. 2008;12:201–203. - PubMed

Publication types

LinkOut - more resources