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Case Reports
. 2015 Jan;63(1):61-3.
doi: 10.4103/0301-4738.151474.

Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony

T Ashwini Kini  1 , V S Prakash, Suresh Puthalath, P L Bhandari
Affiliations
Case Reports

Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony

T Ashwini Kini et al. Indian J Ophthalmol. 2015 Jan.

Abstract

Progressive hemifacial atrophy (PHA) is a disease of unknown etiology affecting one-half of the face. Ocular involvement is uncommon. Atrophy of iris is rare, with only a few cases of partial atrophy being reported in the literature. We report a case of total atrophy of iris and ciliary body with associated ocular hypotony in a 16-year-old girl with PHA. We believe this is the first reported case of complete atrophy of iris and ciliary body in PHA. Ocular hypotony in PHA was thought to be due to intra-ocular inflammation. However in our case it appears to be secondary to severe atrophy of the ciliary body.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Hemifacial atrophy involving the right side of the face
Figure 2
Figure 2
Slit lamp diffuse illumination showing near total iris atrophy with dilated pupil
Figure 3
Figure 3
Fundus photo showing hypotonic maculopathy
Figure 4
Figure 4
Ultrasound biomicroscopy of both eyes showing iris with ciliary body atrophy on the right side
See this image and copyright information in PMC

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