Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2015 Mar 12:2015:bcr2014207663.
doi: 10.1136/bcr-2014-207663.

Sturge-Weber syndrome: oral and extra-oral manifestations

Amitandra Kumar Tripathi  1 , Vivek Kumar  1 , Rahul Dwivedi  2 , Charanjit Singh Saimbi  3
Affiliations
Case Reports

Sturge-Weber syndrome: oral and extra-oral manifestations

Amitandra Kumar Tripathi et al. BMJ Case Rep. .

Abstract

Sturge-Weber syndrome is a rare, congenital, neuro-oculo-cutaneous disorder which is characterised extra-orally by unilateral port wine stains on the face, glaucoma, seizures and mental retardation, and intra-orally by ipsilateral gingival haemangioma which frequently affects the maxilla or mandible. In the present case, a 15-year-old female patient presented with a port wine stain on the right side of the face and glaucoma of the right eye, and intra-orally with gingival haemangioma on the right side of the maxilla.

PubMed Disclaimer

Figures

Figure 1
Figure 1
Port wine stain on the right side of the face.
Figure 2
Figure 2
Dilated blood vessels in the right eye.
Figure 3
Figure 3
(A, B) Unilateral hyperplastic lesions on the right side of the maxilla.
Figure 4
Figure 4
Blanching of lesion under pressure.
Figure 5
Figure 5
Lateral cephalogram showing tram-line calcification in the occipital region.
Figure 6
Figure 6
Postero-anterior view showing tram-line calcification in the parietal region.
Figure 7
Figure 7
CT showing severe alveolar bone loss on the affected side of the oral cavity.
See this image and copyright information in PMC

References

    1. Royle HE, Lapp R, Ferrara ED. The Sturge-Weber syndrome. Oral Surg Oral Med Oral Pathol 1966;22:490–7. 10.1016/0030-4220(66)90429-4 - DOI - PubMed
    1. Neto FXP, Junior MAV, Ximenes LS et al. . Clinical features of Sturge-Weber syndrome. Intl Arch Otorhinolaryngol 2008;12:565–70.
    1. Welty LD. Sturge-Weber syndrome: a case study. Neonatal Netw 2006;25:89–98. 10.1891/0730-0832.25.2.89 - DOI - PubMed
    1. Mukhopadhyay S. Sturge-Weber syndrome: a case report. J Indian Soc Pedod Prev Dent 2008;26:29–30. 10.4103/0970-4388.40319 - DOI - PubMed
    1. Inan CJM. Sturge-Weber syndrome; report of an unusual cutaneous distribution. Brain Develop 1999;21:68–70. 10.1016/S0387-7604(98)00067-9 - DOI - PubMed

Publication types