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Case Reports
. 2015 Apr-Jun;20(2):82-3.
doi: 10.4103/0971-9261.151553.

A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra

Jujju Jacob Kurian  1 , Sudipta Sen  1 , Reju Thomas Joseph  1 , Mandeep Singh Bindra  2
Affiliations
Case Reports

A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra

Jujju Jacob Kurian et al. J Indian Assoc Pediatr Surg. 2015 Apr-Jun.

Abstract

Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation.

Keywords: Bilateral cystic nephroma; Dicer-1 mutation; urethral embryonal rhabdomyosarcoma.

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Conflict of interest statement

Conflict of Interest: None declared.

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