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Case Reports
. 2015 Apr-Jun;9(2):217-9.
doi: 10.4103/1658-354X.152893.

I-gel assisted fiberoptic intubation in a child with Morquio's syndrome

Sangeeta Dhanger  1 , Sethuramachandran Adinarayanan  2 , Stalin Vinayagam  2 , Mohanasundaram Praveen Kumar  2
Affiliations
Case Reports

I-gel assisted fiberoptic intubation in a child with Morquio's syndrome

Sangeeta Dhanger et al. Saudi J Anaesth. 2015 Apr-Jun.

Abstract

Morquio's syndrome, also known as mucopolysaccharidosis type IV is an autosomal recessive disorder, caused by deficiency of n-acetylgalactosamine-6-sulphate. Anesthetic management of this syndrome is a great challenge, especially in pediatric age group as "cannot ventilate, cannot intubate" scenario can be encountered by anesthesiologist due to the possibility of total airway collapse. Herewith, we are reporting a case of child with Morquio's syndrome where I-gel assisted fiber-optic intubation was used for safe endotracheal intubation.

Keywords: Difficult airway; I-gel; Morquio's syndrome; fiber-optic bronchoscope.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Magnetic resonance imaging cervical spine sagittal section, showing cord compression at C1 vertebrae with loss of cerebrospinal fluid space
See this image and copyright information in PMC

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