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Case Reports
. 2015 Feb 27:5:10.
doi: 10.4103/2156-7514.152339. eCollection 2015.

Complete currarino syndrome recognized in adulthood

Affiliations
Case Reports

Complete currarino syndrome recognized in adulthood

Sinan Akay et al. J Clin Imaging Sci. .

Abstract

Currarino syndrome is a hereditary pathology that is characterized by sacrococcygeal bone defect, presacral mass, and anorectal malformation. Sacrococcygeal bone defect is almost always a part of the syndrome. The complete form of this entity displays all three abnormalities and is very uncommon. In this report, we present the magnetic resonance imaging findings of a case with complete form of Currarino syndrome recognized in adulthood.

Keywords: Anorectal; Currarino syndrome; meningocele; sacrococcygeal.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
20-year-old man with anal atresia operation history in childhood diagnosed with Currarino syndrome. (a) T2-weighted sagittal magnetic resonance image shows calibre of one-third of inferior rectum is very thin (thick white arrows), while superior and middle segments of the rectum are dilated (arrowheads). Also, the images demonstrate anterior meningocele (asterisk) at the posterior of the rectum related to spinal canal that originated from the neural foramen of S2 and S3 vertebrae. The lesion is isointense with cerebrospinal fluid. (b) Fat-saturated T2-weighted axial magnetic resonance image shows partial cleft at L5 vertebra corpus (thin white arrow) and dilated rectum in front of it. On (c) T1-weighted and (d) Fat-saturated T2-weighted axial magnetic resonance images, left half of the sacrum is not seen. In this part, spinal canal relationship of anterior meningocele (asterisk) and its indentation to the adjacent rectum is also observed. (e) T2-weighted coronal magnetic resonance images demonstrate the contiguity of the sacral defect and anterior meningocele (asterisk) more clearly (R = rectum, B = bladder).

References

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