Masquerading acidosis after cardiopulmonary bypass: a case of propionic acidemia and congenital heart disease

Abstract

We report the case of a child with both propionic acidemia and cyanotic congenital heart disease. The presence of an underlying inborn error of metabolism confounded the management of this patient in the postoperative period, resulting in therapeutic misdirection until the true etiology of hyperlactemia was recognized.

Keywords: CPB; arterial switch operation; complications; congenital heart disease; congenital heart surgery; inflammatory response; intensive care; metabolism; postoperative care.