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Case Reports
. 2015 Jan-Mar;10(1):18-21.
doi: 10.4103/1817-1745.154321.

Suprasellar arachnoid cyst presenting with bobble-head doll syndrome: Report of three cases

Shighakolli Ramesh  1 , Subodh Raju  1
Affiliations
Case Reports

Suprasellar arachnoid cyst presenting with bobble-head doll syndrome: Report of three cases

Shighakolli Ramesh et al. J Pediatr Neurosci. 2015 Jan-Mar.

Abstract

Suprasellar arachnoid cysts can have varied presentations with signs and symptoms of obstructive hydrocephalus, visual impairment, endocrinal dysfunction, gait ataxia and rarely bobble-head doll movement. The bobble-head doll movement is a rare movement disorder characterized by antero-posterior bobbling of the head and neck on the trunk every 2-3 seconds. We present three cases with bobble-head doll syndrome associated with a large suprasellar arachnoid cyst and obstructive hydrocephalus, which were treated with endoscopic cystoventriculocisternostomy and marsupialization of the cyst.

Keywords: Bobble-head doll syndrome; endoscopic cystoventriculocisternostomy; hydrocephalus; suprasellar arachnoid cyst.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
T1-weighted images coronal: Well-defined cerebrospinal fluid signal intensity in prepontine, interpeduncular, suprasellar, anterior third ventricle with dilatation of third and both lateral ventricles
Figure 2
Figure 2
T1-weighted images axial: Well-marginated cerebrospinal fluid signal intensity cystic lesion in prepontine, interpeduncular, suprasellar, anterior third ventricle with moderate dilatation of third and both lateral ventricles
Figure 3
Figure 3
T1-weighted image axial: Ventricular dilatation has significantly decreased with near normal size ventricles
Figure 4
Figure 4
T2 sagittal: Gross dilatation of body of lateral and third ventricle with fenestrations of cyst at superior and inferior aspect
Figure 5
Figure 5
Cyst bulging into foramen of monro
Figure 6
Figure 6
Thinned out third ventricular floor
Figure 7
Figure 7
Computed tomography scan: Cerebrospinal fluid cystic lesion noted in suprasellar, prepontine, interpendicular, third ventricle with moderate obstructive hydrocephalus. Normal fourth ventricle
Figure 8
Figure 8
Minimal decrease in cerebrospinal fluid density cystic lesion and obstructive hydrocephalus
See this image and copyright information in PMC

References

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