Oral manifestations of Parry-Romberg syndrome: A review of literature

Abstract

Parry-Romberg syndrome (PRS) or progressive facial hemiatrophy is a developmental craniofacial disorder of unknown etiology characterized by a slowly progressive unilateral facial atrophy. It is associated with different systemic manifestations particularly, maxillofacial, neurologic and ophthalmologic abnormalities. Dentists must be aware of PRS to identify this invalidating disorder. In this article, we review the etiology, clinical features (especially craniofacial and dental manifestations) and treatment of PRS. We searched in PubMed line using specific words such as PRS from 2008 to 2014 (August). We identify 14 papers have described oral manifestations of this syndrome. We excluded all the article papers that did not indicate to oral manifestations of PRS.

Keywords: Facial hemiatrophy; Parry–Romberg syndrome; oral manifestations.

Figure 1

Marked hypoplasia of the left side of the face with deviation of lips and nose toward left side and notching of lips and nose with exposure of teeth. Alopecia in left eyebrow region (Deshingkar et al. 2012)

Figure 2

Unilateral atrophy of tongue papillae of left side (Deshingkar et al. 2012)

Figure 3

Orthopantomograph showing retarded eruption pattern of teeth on left side compared to that of right side. Decreased vertical height of ramus along with loss of gonial angle prominence on the affected side (Deshingkar et al. 2012)