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Case Reports
. 2015 Mar;23(1):48-51.
doi: 10.4250/jcu.2015.23.1.48. Epub 2015 Mar 30.

Double chambered right ventricle with ventricular septal defect in adults: case series and review of the literature

Sherif Moustafa  1 , David J Patton  2 , Nanette Alvarez  3 , Mansour Al Shanawani  4 , Khalid AlDossari  4 , Michael S Connelly  3 , Timothy Prieur  3 , Farouk Mookadam  5
Affiliations
Case Reports

Double chambered right ventricle with ventricular septal defect in adults: case series and review of the literature

Sherif Moustafa et al. J Cardiovasc Ultrasound. 2015 Mar.

Abstract

Double-chambered right ventricle (DCRV) is an uncommon congenital anomaly in which anomalous muscle bands divide the right ventricle into two chambers; a proximal high-pressure and distal low-pressure chamber. It may be associated with mid right ventricular obstruction. It is commonly associated with other congenital anomalies, most frequently perimembranous ventricular septal defect (PM-VSD). We herein present 5 adult patients with concomitant DCRV and PM-VSD who varied in their symptomatic presentations and the ways of management.

Keywords: Double chambered right ventricle; Echocardiography; Magnetic resonance; Ventricular septal defect.

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Figures

Fig. 1
Fig. 1. A: Transesophageal echocardiogram mid esophageal view showing muscle band in the right ventricular outflow tract (arrow). B, C, and D: Transthoracic echocardiogram short axis views showing right ventricular muscle band (arrow). C: Posterior pericardial effusion was noted. E: Transesophageal echocardiogram mid esophageal view showing muscle band in the right ventricular outflow tract (left, black arrow) with color turbulence across (right). Pulmonic valve was shown (white arrow). LA: left atrium, LV: left ventricle, PA: pulmonary artery, RV: right ventricle, RVOT: right ventricular outflow tract.
Fig. 2
Fig. 2. A and B: Cardiac magnetic resonance: sagittal steady-state free precession views demonstrating prominent right ventricular outflow tract muscle bundles causing significant dephasing (arrow). C, D, and E: Cardiac magnetic resonance: sagittal steady-state free precession views demonstrating prominent right ventricular outflow tract muscle bundles without significant dephasing (arrow). C: Pericardial effusion was noted as well. LV: left ventricle, RV: right ventricle, PE: pericardial effusion.
See this image and copyright information in PMC

References

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