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. 2015:2015:601038.
doi: 10.1155/2015/601038. Epub 2015 Apr 1.

Ewing's Sarcoma of the Kidney Complicated by a Wunderlich Syndrome

Mihai Razvan Manescu  1 , Achraf Sahyoun  1 , Nicolas Froment  2 , Nicolae Crisan  3 , Vincent Girot  1
Affiliations

Ewing's Sarcoma of the Kidney Complicated by a Wunderlich Syndrome

Mihai Razvan Manescu et al. Case Rep Urol. 2015.

Abstract

The Wunderlich syndrome found after the rupture of primitive renal Ewing's sarcoma is not a situation that we find often in everyday practice. The clinical findings are not specific, which is why the differential diagnosis must be made with a multitude of benign and malignant renal masses until the correct diagnosis can be made by the pathologist. The CT and MRI images are not characteristic. One treatment option is the multidisciplinary approach; however, the prognosis remains poor for patients with metastatic disease.

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Figures

Figure 1
Figure 1
(a) The coronal reconstructed CT image shows a large solid heterogeneous mass without calcifications in the left kidney and also a perirenal hematoma. (b) The axial CT image of the upper abdomen reveals a large solid heterogeneous mass measuring 7 × 6.7 in the left kidney and also a perirenal hematoma.
Figure 2
Figure 2
(a) Small blue cells arranged in Homer-Wright rosettes; (b) tumor cells and rosettes, numerous atypical mitoses; (c) tumor cells labeled with anti-S100 protein antibody.
See this image and copyright information in PMC

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