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Case Reports
. 2013 Mar 1;29(1):42-4.
doi: 10.5152/UCD.2013.11. eCollection 2013.

An atypically localized gastrointestinal stromal tumor: a case report of pancreas gastrointestinal stromal tumor

Kürşat Rahmi Serin  1 , Metin Keskin  1 , Mine Güllüoğlu  2 , Ali Emre  1
Affiliations
Case Reports

An atypically localized gastrointestinal stromal tumor: a case report of pancreas gastrointestinal stromal tumor

Kürşat Rahmi Serin et al. Ulus Cerrahi Derg. .

Abstract

Gastrointestinal stromal tumors (GISTs) are the most common mesenchymal tumors of the gastrointestinal tract. They can arise from any part of the tract as well as the omentum, mesentery or retroperitoneum. In this study, we present a case of a GIST originating from an extraordinary site, the pancreas. Evaluation of 30-year-old man with complaints of abdominal distension revealed a cystic, distal pancreatic lesion 13 cm in diameter. There were no intra-abdominal or distant organ metastases. The patient was operated with a diagnosis of cystic pancreas tumor, distal pancreatectomy and splenectomy was performed. The lesion was diagnosed as gastrointestinal stromal tumor upon histopathological examination. He was discharged on the sixth postoperative day without any complications and is being followed up for 21 months without systemic or local recurrence. Extragastrointestinal GISTs are reported rarely. To our knowledge, only one pancreatic GIST has been reported previously in the English literature.

Keywords: Gastrointestinal stromal tumour; extragastrointestinal; pancreas.

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Figures

Figure 1.
Figure 1.
CT image showing a cystic mass that is 13cm in size, originating from the distal pancreas, located behind the stomach without any evidence of gastric invasion and containing areas of necrosis and septa
Figure 2.
Figure 2.
Cells within the neoplastic area containing necrosis and hemorrhage foci and C-kit positivity
See this image and copyright information in PMC

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