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Case Reports
. 2015 Mar;9(3):OD08-9.
doi: 10.7860/JCDR/2015/11919.5700. Epub 2015 Mar 1.

Cronkhite-Canada Syndrome (CCS)-A Rare Case Report

Subrata Chakrabarti  1
Affiliations
Case Reports

Cronkhite-Canada Syndrome (CCS)-A Rare Case Report

Subrata Chakrabarti. J Clin Diagn Res. 2015 Mar.

Abstract

Cronkhite-Canada syndrome (CCS) is an extremely rare non-inherited condition characterized by gastrointestinal hamartomatous polyposis, alopecia, onychodystrophy, hyperpigmentation, weight loss and diarrhoea. The aetiology is probably autoimmune and diagnosis is based on history, physical examination, endoscopic findings of gastrointestinal polyposis, and histology. The disease is very rare; approximately 450 cases of CCS have been reported worldwide. The author reports a case of CCS in an elderly Indian male.

Keywords: Alopecia; Hyperpigmentation; Onychodystrophy; Polyposis.

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Figures

[Table/Fig-1]:
[Table/Fig-1]:
Showing hyperpigmentation in hands and feet including palmar surfaces
[Table/Fig-2]:
[Table/Fig-2]:
Showing hyperpigmentation in soles
[Table/Fig-3]:
[Table/Fig-3]:
Showing onychodystrophy in fingers
[Table/Fig-4]:
[Table/Fig-4]:
Showing onychodystrophy in toes
[Table/Fig-5]:
[Table/Fig-5]:
Showing diffuse polyposis in small intestine
[Table/Fig-6]:
[Table/Fig-6]:
Showing diffuse polyposis in colon
See this image and copyright information in PMC

References

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