Aplasia cutis congenita scalp presenting with life threatening hemorrhage: a case report
- PMID: 26023367
- PMCID: PMC4420308
Aplasia cutis congenita scalp presenting with life threatening hemorrhage: a case report
Abstract
Aplasia cutis congenita is a rare congenital anomaly characterized by the absence of a patch of skin since birth. It may lead to life threatening complications at times. A 5-day-old neonate with Aplasia cutis congenita was received in a state of shock due to tremendous blood loss from the superior sagittal sinus. The neonate was resuscitated immediately followed by closure of the superior sagittal sinus and flap coverage to the defect as a life saving procedure.
Keywords: Aplasia cutis congenita; Hemorrhage; Superior sagittal sinus.
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References
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- Chitnis MR, Carachi R, Galea P. Familial Aplasia Cutis Congenita. Eur J Pediatric Surg 1996;6:100-1. - PubMed
-
- Kim CS, Tatum SA, Rodziewicz G. Scalp Aplasia Cutis Congenita Presenting With Sagittal Sinus Hemorrhage. Arch Otolaryngol Head Neck Surg 2001;127:71-4. - PubMed
-
- Schneider BM, Berg RA, Kaplan AM. Aplasia Cutis Congenita Complicated by Sagittal Sinus Hemorrhage. Pediatr 1980;66:948-50. - PubMed
-
- Vijayashankar. Aplasia cutis congenita: A case report. Dermatol Onlin J 2005;11:28. - PubMed
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