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Case Reports
. 2012 Jan 1;1(1):8.
eCollection 2012 Jan-Mar.

Aplasia cutis congenita scalp presenting with life threatening hemorrhage: a case report

Affiliations
Case Reports

Aplasia cutis congenita scalp presenting with life threatening hemorrhage: a case report

Farrukh Mahmood et al. J Neonatal Surg. .

Abstract

Aplasia cutis congenita is a rare congenital anomaly characterized by the absence of a patch of skin since birth. It may lead to life threatening complications at times. A 5-day-old neonate with Aplasia cutis congenita was received in a state of shock due to tremendous blood loss from the superior sagittal sinus. The neonate was resuscitated immediately followed by closure of the superior sagittal sinus and flap coverage to the defect as a life saving procedure.

Keywords: Aplasia cutis congenita; Hemorrhage; Superior sagittal sinus.

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Figures

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Figure 1: Wound Debridement and repair of superior sagittal sinus
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Figure 2: Transposition Flap Marking
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Figure 3: Flap elevated
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Figure 4: Flap inset
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Figure 5: The donor site closure with split thickness skin graf

References

    1. Chitnis MR, Carachi R, Galea P. Familial Aplasia Cutis Con­genita. Eur J Pediatric Surg 1996;6:100-1. - PubMed
    1. Kim CS, Tatum SA, Rodziewicz G. Scalp Aplasia Cutis Con­genita Presenting With Sagittal Sinus Hemorrhage. Arch Otolaryngol Head Neck Surg 2001;127:71-4. - PubMed
    1. Schneider BM, Berg RA, Kaplan AM. Aplasia Cutis Conge­nita Complicated by Sagittal Sinus Hemorrhage. Pediatr 1980;66:948-50. - PubMed
    1. Vijayashankar. Aplasia cutis congenita: A case report. Der­matol Onlin J 2005;11:28. - PubMed

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