Atypical paracaval recurrence of uterine endometrial stromal sarcoma: a case report

Abstract

Endometrial stromal sarcomas are rare uterine malignancies with a high capacity for recurrence, even in cases diagnosed at an early stage of the disease. Recurrence is usually confined to the pelvic space but sometimes accelerated growth and extension into the upper abdomen can be found. In such cases, an aggressive surgical approach might be needed in order to provide complete resection of the recurrent tumor. We present the case of a 51-year-old patient who was diagnosed with an atypical spindle-shaped recurrence stretching from the pelvic floor to the right renal hilum along the inferior vena cava following total interadnexial hysterectomy for a presumed benign uterine tumor. An R0 resection of the recurrent tumor was performed and the histopathological study revealed the presence of a low-grade endometrial stromal sarcoma.

Keywords: Endometrial stromal sarcoma; case report; complete resection; paracaval recurrence.