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. 2015 Jun;5(3):469-71.
doi: 10.3978/j.issn.2223-4292.2014.11.17.

Dyke-Davidoff-Masson syndrome: imaging features with illustration of two cases

Richa Arora  1 , Jyotsna Y Rani  1
Affiliations

Dyke-Davidoff-Masson syndrome: imaging features with illustration of two cases

Richa Arora et al. Quant Imaging Med Surg. 2015 Jun.

Abstract

Dyke-Davidoff-Masson syndrome is a rare entity characterized by hemi cerebral atrophy/hypoplasia secondary to brain insult in fetal or early childhood period along with ipsilateral compensatory osseous hypertrophy and contralateral hemiparesis. We present two cases of this uncommon condition and discuss its imaging features, differential diagnosis, treatment options and prognosis.

Keywords: Hemiatrophy; magnetic resonance imaging (MRI); refractory seizures.

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Figures

Figure 1
Figure 1
Axial FLAIR sequence of MRI brain showing atrophy of left cerebral hemisphere with atrophied left side of midbrain with thickened calvarium. MRI, magnetic resonance imaging.
Figure 2
Figure 2
Axial T2 weighted sequence showing left hemi cerebral atrophy.
Figure 3
Figure 3
Coronal T2 weighted images showing hemi atrophy of right cerebral hemisphere with (A) enlarged right frontal sinus, (B) sphenoid sinus and (C) elevated sphenoid ridge on the right.
Figure 4
Figure 4
(A-C) Axial T2 weighted and (B) FLAIR sequence showing (A&B) right hemi cerebral atrophy with enlarged right frontal sinus.
See this image and copyright information in PMC

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