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Case Reports
. 2015 May-Aug;8(2):161-3.
doi: 10.4103/0974-2069.154154.

Isolation of the right subclavian artery in a patient with d-transposition of the great arteries

Alisa Arunamata  1 , Stanton B Perry  1 , Alaina K Kipps  1 , Shreyas S Vasanawala  2 , David M Axelrod  1
Affiliations
Case Reports

Isolation of the right subclavian artery in a patient with d-transposition of the great arteries

Alisa Arunamata et al. Ann Pediatr Cardiol. 2015 May-Aug.

Abstract

Isolation of the right subclavian artery (RSCA) is rare, and this finding in association with d-transposition of the great arteries (d-TGA) is extremely unusual. We present a case of an isolated RSCA in a newborn with d-TGA in whom the clinical presentation was diagnostic. We discuss the imaging modalities used to confirm the diagnosis, the embryological basis of the finding, and the surgical repair.

Keywords: Anomalous origin of right subclavian artery; congenital heart disease; isolated right subclavian artery; transposition of the great arteries.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Transthoracic echocardiogram demonstrating a vessel arising from the proximal right pulmonary artery (RPA) and coursing superior and rightward, suggestive of an anomalous origin of the right subclavian artery (RSCA). AO = Aorta
Figure 2
Figure 2
Thin-slab three-dimensional surface rendering magnetic resonance imaging confirming the isolated RSCA from a right ductus arteriosus (DA) arising from the proximal RPA
Figure 3
Figure 3
Intraoperative image of the RSCA connected to the RPA via a long segment of ductal tissue. RV = Right ventricle
Figure 4
Figure 4
(a) Diagram of the normal embryological origin of the RSCA from the seventh (VII) intersegmental artery with subsequent cranial migration, and dissolution (in black) of the R-PDA and right fourth (IV) aortic arch (R-arch). (b) Isolation of the RSCA occurs when there is dissolution (in black) of the right IV aortic arch but persistence of the right sixth (VI) arch from which the R-PDA and RPA take their origin. L-arch = Left aortic arch, LCCA = left common carotid artery, L-PDA = left ductus arteriosus, LSVC = left subclavian artery, LPA = left pulmonary artery, RCCA = right common carotid artery
See this image and copyright information in PMC

References

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