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Case Reports
. 2015 Jul 15:2015:bcr2015211166.
doi: 10.1136/bcr-2015-211166.

Unicuspid aortic valve presenting with cardiac arrest in an adolescent

Tara Connelly  1 , Walenty Kolcow  2 , Yvonne Smyth  3 , David Veerasingham  2
Affiliations
Case Reports

Unicuspid aortic valve presenting with cardiac arrest in an adolescent

Tara Connelly et al. BMJ Case Rep. .

Erratum in

  • Correction.
    [No authors listed] [No authors listed] BMJ Case Rep. 2015 Jul 27;2015:bcr2015211166corr1. doi: 10.1136/bcr-2015-211166corr1. BMJ Case Rep. 2015. PMID: 26216928 Free PMC article. No abstract available.

Abstract

Unicuspid aortic valve (UAV) is a rare congenital anomaly typically affecting patients in their fourth and fifth decades and presenting with signs of heart failure. Our case is one of a previously asymptomatic teenage girl with a UAV, who presented with cardiac arrest and was successfully treated. Only two other similar cases have been reported in the literature, both were of slightly older male patients. Our case highlights the morbidity associated with the anomaly supporting the need for careful assessment of the valve in cases where UAV is suspected.

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Figures

Figure 1
Figure 1
The prolapsing valve leaflet is located below the aortic annulus in LVOT (left ventricle outflow tract).
Figure 2
Figure 2
Transthoracic echocardiogram demonstrating severe aortic regurgitation with eccentric jet (long axis view).
Figure 3
Figure 3
Visible stenotic unicuspid aortic valve with a single commissure (‘C’). The 2 raphae are annotated with ‘R.’
Figure 4
Figure 4
A severely dilated left ventricle in association with unicuspid aortic valve (UAV) is demonstrated.
Figure 5
Figure 5
Image taken in systole.
Figure 6
Figure 6
Intraoperative image of unicuspid aortic valve.
Figure 7
Figure 7
Pathology specimen of unicuspid aortic valve.
See this image and copyright information in PMC

References

    1. Mookadam F, Thota VR, Garcia-Lopez AM et al. . Unicuspid aortic valve in adults: a systematic review. J Heart Valve Dis 2010;19:79–85. - PubMed
    1. Falcone MW, Roberts WC, Morrow AG et al. . Congenital aortic stenosis resulting from a unicommisssural valve. Clinical and anatomic features in twenty-one adult patients. Circulation 1971;44:272–80. 10.1161/01.CIR.44.2.272 - DOI - PubMed
    1. Murphy BA, Groban L, Kon ND. Diagnosis of a unicuspid aortic valve using transesophageal echocardiography. J Cardiothorac Vasc Anesth 2003;17:82–3. 10.1053/jcan.2003.15 - DOI - PubMed
    1. Ucak A, Inan K, Onan B et al. . Left sinus of valsalva aneurysm in an adult with congenital unicuspid aortic valve. Int J Cardiol 2011;149:e21–23. 10.1016/j.ijcard.2009.03.039 - DOI - PubMed
    1. Ohata T, Miyamoto Y, Takahashi T et al. . Sinus of Valsalva aneurysm with congenital aortic stenosis and aortic coarctation. Asian Cardiovasc Thorac Ann 2004;12:75–7. 10.1177/021849230401200118 - DOI - PubMed

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