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Case Reports
. 2014 Jun;11(2):210-2.
doi: 10.5114/kitp.2014.43853. Epub 2014 Jun 29.

Anomalous origin of circumflex coronary artery from right pulmonary artery in a hypoplastic left heart syndrome child

Radoslaw Jaworski  1 , Andrzej Kansy  2 , Przemysław Łaniewski-Wołłk  3
Affiliations
Case Reports

Anomalous origin of circumflex coronary artery from right pulmonary artery in a hypoplastic left heart syndrome child

Radoslaw Jaworski et al. Kardiochir Torakochirurgia Pol. 2014 Jun.

Abstract
in English, Polish

We describe the case of a newborn with hypoplastic left heart syndrome (HLHS) and aberrant origin of the circumflex coronary artery from the right pulmonary artery. The patient underwent a modified Norwood procedure with direct reimplantation of the circumflex coronary artery to the neo-aorta, but died on the 5(th) postoperative day because of myocardial failure. Detailed assessment of coronary arteries as part of the routine echocardiographic evaluation of HLHS and intraoperative inspection of them is crucial.

W pracy opisano przypadek kliniczny noworodka z zespołem hipoplazji lewego serca i nieprawidłowym odejściem gałęzi okalającej lewej tętnicy wieńcowej od prawej tętnicy płucnej. U dziecka wykonano operację Norwooda w modyfikacji Sano z przeszczepieniem gałęzi okalającej lewej tętnicy wieńcowej do neoaorty. W 5. dobie pooperacyjnej dziewczynka zmarła z powodu niewydolności serca. Dokładna ocena przebiegu tętnic wieńcowych u dzieci z zespołem hipoplazji lewego serca jest w planowaniu zabiegu operacyjnego niezwykle istotna.

Keywords: congenital heart disease; coronary artery anomaly; hypoplastic left heart syndrome.

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Figures

Fig. 1
Fig. 1
Circumflex coronary artery dissected from right pulmonary artery with a cuff during Norwood procedure (arrow; operator view)
Fig. 2
Fig. 2
Circumflex coronary artery (arrows) after reimplantation into the posterior wall of the neoaorta (operator views): A) from neoaorta lumen; B) after neoaorta reconstruction
See this image and copyright information in PMC

References

    1. Nathan M, Emani S, Marx G, Pigula F. Anomalous left coronary artery arising from the pulmonary artery in hypoplastic left hearts: Case series and review of literature. J Thorac Cardiovasc Surg. 2011;142:225–227. - PubMed
    1. Baffa JM, Chen SL, Guttenberg ME, Norwood W, Weinberg PM. Coronary artery abnormalities and right ventricular histology in hypoplastic left heart syndrome. J Am Coll Cardiol. 1992;20:350–358. - PubMed
    1. Sarris GE, Drummond-Webb JJ, Ebeid MR, Latson LA, Mee RB. Anomalous origin of left coronary from right pulmonary artery in hypoplastic left heart syndrome. Ann Thorac Surg. 1997;64:836–838. - PubMed
    1. Malec E, Mroczek T, Pajak J, Zajac A, Kolcz J, Januszewska K. Hypoplastic left heart syndrome with an anomalous origin of the left coronary artery. Ann Thorac Surg. 2001;72:2129–2130. - PubMed
    1. Nosal’ M, Omeje IC, Poruban R. Hypoplastic left heart syndrome with anomalous origin of left coronary artery from the right pulmonary artery: successful surgical treatment in a neonate. Eur J Cardiothorac Surg. 2005;28:497–498. - PubMed

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