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. 2015:2015:134123.
doi: 10.1155/2015/134123. Epub 2015 Aug 3.

CT Imaging of Craniofacial Fibrous Dysplasia

Zerrin Unal Erzurumlu  1 , Peruze Celenk  2 , Emel Bulut  3 , Yakup Sancar Barıs  4
Affiliations

CT Imaging of Craniofacial Fibrous Dysplasia

Zerrin Unal Erzurumlu et al. Case Rep Dent. 2015.

Abstract

Fibrous dysplasia is a benign fibroosseous bone dysplasia that can involve single (monostotic) or multiple (polyostotic) bones. Monostotic form is more frequent in the jaws. It is termed as craniofacial fibrous dysplasia, when it involves, though rarely, adjacent craniofacial bones. A 16-year-old girl consulted for a painless swelling in the right posterior mandible for two years. Panoramic radiography revealed ground-glass ill-defined lesions in the three different regions of the maxilla and mandible. Axial CT scan (bone window) showed multiple lesions involving skull base and facial bones. Despite lesions in the skull base, the patient had no abnormal neurological findings. The lesion was diagnosed as fibrous dysplasia based on radiological and histopathological examination. In this paper, CT findings and differential diagnosis of CFD are discussed. CT is a useful imaging technique for CFD cases.

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Figures

Figure 1
Figure 1
Expansive mass of the right maxilla.
Figure 2
Figure 2
Panoramic radiography shows ground-glass ill-defined lesions in the three different regions of the maxilla and mandible.
Figure 3
Figure 3
(a), (b), (c), (d), (e), (f) Axial CT scans (bone window) showing multiple bone lesions involving skull base and facial bones.
Figure 4
Figure 4
(a) Sagittal reformatted CT images showing expansive mixed lesions involving the mandible, temporal bone, and zygomatic bone. (b) 3D CT images showing the CFD affecting the right side of the mandible (white arrow), in the right maxilla (black arrow head), in the right lateral wall of the orbit (black arrow).
Figure 5
Figure 5
Histopathology demonstrates immature bone anastomosis, forming at the fibrous stroma rich of cellular and vascular structure. Vascular structure (black arrow), osteocyte (small black arrow), osteoid matrix (blue arrow), and fibrous stroma (two-sided arrow) are shown (HE ×200).
See this image and copyright information in PMC

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