Case Reports
The Adverse Effects of Pregnancies Complicated by Hemoglobin H (HBH) Disease
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- PMID: 26351505
- PMCID: PMC4539740
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Case Reports
The Adverse Effects of Pregnancies Complicated by Hemoglobin H (HBH) Disease
Iran J Pathol.
2015 Fall.
Abstract
Hemoglobin (Hb) H disease is a moderate form of α- thalassemia resulting from various genetic defects. HbH disease is not necessarily a benign disorder as has been generally thought. We present hereby a 25- year-old Iranian pregnant woman whom referred to our hospital for blood transfusion. She exhibited the clinical and hematological manifestation of HbH disease. Her father carries a common α-thalassemia deletion while her mother was normal in the hematological profile. The object of this report was to provide information about pregnancies affected by HbH disease.
Keywords: Hemoglobin H; Iran; Pregnancy.
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