Omental rhabdomyosarcoma (primary rhabdoid tumor of greater omentum): a rare case report

Abstract

The greater omentum is an uncommon location for primary tumors. Metastatic tumors of the omentum are common. In contrast, primary tumors of the omentum are very rare. Sporadic cases of primary rhabdomyosarcoma (RMS) arising in the abdomen have been reported, but these cases are limited almost exclusively to the pediatric population. We report a well-documented case of primary intra-abdominal RMS in a 21-year-old man who presented with complaints of abdominal pain and lump in left hypochondrium region. Imaging revealed it to be a large mass in the left hypochondrium region displacing the bowel loops. Further investigations revealed omental RMS. The mass had originated from the greater omentum and was excised. Our case is doing well and is presently receiving chemotherapy.

Keywords: Greater omentum; Rhabdomyosarcoma.

Fig. 1

Showing a large well defined mass of 9.8 × 7.4 cms along with displacement of the bowel loops

Fig. 2

Intra operative finding of a large omental tumor in the left hypochondrium region with areas of ulceration

Fig. 3

H and E; 10 × 10 X shows malignant round cell tumor arranged in sheets admixed with areas of necrosis

Fig. 4

Immunohistochemistry, 10 × 10 X shows tumor cells showing desmin positivity

Fig. 5

Immunohistochemistry 10 × 10 X shows tumor cells are negative for pancytokeratin