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Review
. 2015 Sep;32(3):267-70.
doi: 10.4274/tjh.2013.0428.

Portal Vein Thrombosis of a Newborn with Corrected Total Anomalous Pulmonary Venous Return

Ufuk Çakır  1 , Dilek Kahvecioğlu, Serdar Alan, Ömer Erdeve, Begüm Atasay, Tayfun Uçar, Saadet Arsan, Hasan Çakmaklı, Mehmet Ertem, Semra Atalay
Affiliations
Review

Portal Vein Thrombosis of a Newborn with Corrected Total Anomalous Pulmonary Venous Return

Ufuk Çakır et al. Turk J Haematol. 2015 Sep.

Abstract
in English, Turkish

Total anomalous pulmonary venous return (TAPVR) is a rare and frequently isolated defect identified in 1% to 3% of all congenital heart diseases. To the best of our knowledge, portal vein thrombosis (PVT) associated with TAPVR has not been reported in the literature. We report a successfully managed PVT in a newborn with infracardiac-type TAPVR and review the literature. Anticoagulation therapies were used during the neonatal period to prevent thrombus progression. PVT should be kept in mind in TAPVR patients who have open heart repair with total correction. The treatment in each neonate should be individualized with consideration of the risk/benefit ratio.

Total anormal pulmoner venöz dönüş (TAPVD) anomalisi nadir ve çoğunlukla izole bir durumdur, bütün konjenital kalp hastalıklarının %1-3’ünü oluşturur. Bildiğimiz kadarıyla, TAPVD anomalisi ile ilişkili portal ven trombozu (PVT) literatürde daha önce yayınlanmamıştır. Burada başarı ile tedavi edilen infrakardiak tipte TAPVD anomalisine eşlik eden PVT’li bir yenidoğan olgusu literatür bilgileri ışığında sunulmaktadır. Tromboz progresyonunu engellemek için yenidoğan dönemi boyunca antikoagülan tedaviler uygulanmıştır. PVT, TAPVD anomalisi olan ve tam düzeltici açık kalp onarımı yapılan hastalarda akılda tutulmalıdır. Her bir yenidoğan için tedavi, risk ve yarar göz önünde tutularak bireyselleştirilmelidir.

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Conflict of interest statement

Conflict of Interest Statement

The authors of this paper have no conflicts of interest, including specific financial interests, relationships, and/or affiliations relevant to the subject matter or materials included.

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References

    1. Chen YY, Hsu CY. Prenatal diagnosis and antenatal history of total anomalous pulmonary venous return. Taiwan J Obstet Gynecol. 2006;45:283–285. - PubMed
    1. Kohli V, Sachdev MS, Joshi RK, Joshi R. Post-op systemic hypertensive crises in an infant with total anomalous pulmonary venous connection. Indian J Pediatr. 2009;76:755–756. - PubMed
    1. Jang SI, Song JY, Kim SJ, Choi EY, Shim WS, Lee C, Lim HG, Lee CH. The recent surgical result of total anomalous pulmonary venous return. Korean Circ J. 2010;40:31–35. - PMC - PubMed
    1. Frommelt PC, Sheridan DC, Deatsman S, Yan K, Simpson P, Frommelt MA, Litwin SB, Tweddell JS. Unobstructive total anomalous pulmonary venous return: impact of early elective repair on the need for prolonged mechanical ventilatory support. Pediatr Cardiol. 2010;31:1191–1197. - PubMed
    1. Williams S, Chan AK. Neonatal portal vein thrombosis: diagnosis and management. Semin Fetal Neonatal Med. 2011;16:329–339. - PubMed

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