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Case Reports
. 2015 Fall;9(4):357-9.
doi: 10.1097/ICB.0000000000000236.

CONGENITAL MACROVESSEL ASSOCIATED WITH CYSTOID MACULAR EDEMA AND AN IPSILATERAL INTRACRANIAL VENOUS MALFORMATION

Christian J Sanfilippo  1 , David Sarraf
Affiliations
Case Reports

CONGENITAL MACROVESSEL ASSOCIATED WITH CYSTOID MACULAR EDEMA AND AN IPSILATERAL INTRACRANIAL VENOUS MALFORMATION

Christian J Sanfilippo et al. Retin Cases Brief Rep. 2015 Fall.

Abstract

Background/purpose: To report a case of congenital retinal macrovessel associated with cystoid macular edema and an ipsilateral intracranial venous malformation.

Methods: Case report.

Results: A 58-year-old woman with decreased vision was found to have a congenital retinal venous macrovessel associated with cystoid macular edema because of tributary venous occlusion. The patient underwent neuroimaging and an ipsilateral venous malformation of the frontal lobe was discovered.

Conclusion: Congenital retinal macrovessel can occasionally be complicated by vascular occlusion and macular edema. The authors report a case of congenital retinal macrovessel associated with an intracranial venous malformation. Clinicians should be aware of this potential association, and further studies are warranted.

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Conflict of interest statement

None of the authors have any financial/conflicting interests to disclose.

Figures

Fig. 1
Fig. 1
Fluorescein angiogram montage showing the course of the large abnormal macrovessel as it crosses the horizontal raphe. Note the absence of abnormal arterial–venous communications.
Fig. 2
Fig. 2
A. Fundus photograph at presentation (A) and a magnified view of the macula (B) showing the abnormally sheathed venous tributary (arrow), and magnified fluorescein angiogram of the macula (C) showing decreased flow through the sheathed tributary (arrow) and capillary bed abnormalities associated with the macrovessel.
Fig. 3
Fig. 3
A. Fundus photograph at the 2-month follow-up visit (A) and a magnified view of the macula (B) showing resolution of the venous sheathing (arrow) and magnified fluorescein angiogram of the macula (C) showing improved flow through the previously sheathed tributary (arrow).
Fig. 4
Fig. 4
A. Spectral domain optical coherence tomography at presentation showing severe cystoid macular edema. B. Spectral domain optical coherence tomography at 2-month follow-up showing resolution of cystoid macular edema.
Fig. 5
Fig. 5
Magnetic resonance imaging with contrast of the brain showing a venous malformation in the left frontal lobe (arrow).
See this image and copyright information in PMC

References

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