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Case Reports
. 2015 Oct;19(4):359-63.
doi: 10.1055/s-0034-1395791. Epub 2014 Nov 14.

Cochlear Implantation in Isolated Large Vestibular Aqueduct Syndrome: Report of Three Cases and Literature Review

Rabindra Pradhananga  1 , Kiran Natarajan  2 , AmarNath Devarasetty  2 , Mohan Kameswaran  3
Affiliations
Case Reports

Cochlear Implantation in Isolated Large Vestibular Aqueduct Syndrome: Report of Three Cases and Literature Review

Rabindra Pradhananga et al. Int Arch Otorhinolaryngol. 2015 Oct.

Abstract

Introduction Large vestibular aqueduct syndrome (LVAS) is characterized by the enlargement of the vestibular aqueduct associated with sensorineural hearing loss. It is the most common radiographically detectable inner ear anomaly in congenital hearing loss. LVAS may occur as an isolated anomaly or in association with other inner ear malformations. Objective To report three cases of isolated LVAS with a focus on preoperative assessment, surgical issues, and short-term postoperative follow-up with preliminary auditory habilitation outcomes. Resumed Report One girl and two boys with LVAS were assessed and cochlear implantation was performed for each. Various ways of intraoperative management of cerebrospinal fluid gusher and postoperative care and outcomes are reported. Conclusion Cochlear implantation in the deaf children with LVAS is feasible and effective.

Keywords: CSF gusher; cochlear implantation; large vestibular aqueduct.

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Figures

Fig. 1
Fig. 1
Computed tomography scan of case 1 showing large vestibular aqueduct.
Fig. 2
Fig. 2
Computed tomography scan of case 2 showing large vestibular aqueduct.
Fig. 3
Fig. 3
Computed tomography scan of case 3 showing bilateral large vestibular aqueduct.
See this image and copyright information in PMC

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