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. 2015:2015:205972.
doi: 10.1155/2015/205972. Epub 2015 Sep 29.

Original Solution for Middle Ear Implant and Anesthetic/Surgical Management in a Child with Severe Craniofacial Dysmorphism

Giovanni Bianchin  1 , Lorenzo Tribi  1 , Aronne Reverzani  2 , Patrizia Formigoni  1 , Valeria Polizzi  1
Affiliations

Original Solution for Middle Ear Implant and Anesthetic/Surgical Management in a Child with Severe Craniofacial Dysmorphism

Giovanni Bianchin et al. Case Rep Otolaryngol. 2015.

Abstract

We describe the novel solution adopted in positioning middle ear implant in a child with bilateral congenital aural atresia and craniofacial dysmorphism that have posed a significant challenge for the safe and correct management of deafness. A five-year-old child, affected by a rare congenital disease (Van Maldergem Syndrome), suffered from conductive hearing loss. Conventional skin-drive bone-conduction device, attached with a steel spring headband, has been applied but auditory restoration was not optimal. The decision made was to position Vibrant Soundbridge, a middle ear implant, with an original surgical application due to hypoplasia of the tympanic cavity. Intubation procedure was complicated due to child craniofacial deformities. Postoperative hearing rehabilitation involved a multidisciplinary team, showing improved social skills and language development.

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Figures

Figure 1
Figure 1
Brain MRI.
Figure 2
Figure 2
CT scan.
Figure 3
Figure 3
Middle ear implant application. The FMT was placed to the long apophysis of the incus with superior orientations.
See this image and copyright information in PMC

Comment in

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