[Atypical coarctation of the thoracic aorta with fibromuscular dysplasia--report of a successful surgical repair and review of the literature]

Abstract

We report a case of 14-year-old woman of fibromuscular dysplasia (FMD) with involvement of the thoracic aorta. Our case is characterized by a segmental stenosis of the thoracic aorta with multiple systemic arterial branch lesions. Atypical coarctation of the thoracic aorta was replaced with Dacron woven graft and the specimen of the lesion demonstrated medial fibroplasia. There have been reported only 9 cases of FMD of the aorta so far and all were female except one case. This report is the first case report of FMD of the thoracic aorta.