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. 2016 Apr;12(2):238-40.
doi: 10.3988/jcn.2016.12.2.238. Epub 2015 Nov 4.

Immunoglobulin G4-Related Hypertrophic Pachymeningitis Mimicking Chiari Malformation

Sung Hee Kim  1 , Ji Soo Kim  2
Affiliations

Immunoglobulin G4-Related Hypertrophic Pachymeningitis Mimicking Chiari Malformation

Sung Hee Kim et al. J Clin Neurol. 2016 Apr.
No abstract available

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Conflict of interest statement

Conflicts of Interest: The authors have no financial conflicts of interest.

Figures

Fig. 1
Fig. 1. Serial brain MRI. A: Initial MRI without a contrast agent performed 3 months after symptom onset revealed a cerebellar tonsillar herniation at 5 mm below the foramen magnum, which was consistent with Chiari malformation type I. B: Follow-up MRI performed 5 months later with gadolinium enhancement disclosed hypertrophic pachymeningitis consisting of diffusely thickened dura mater and space-occupying nodular lesions compressing the left pontine tegmentum and right acoustic meatus. C: MRI performed 3 months after steroid treatment revealed marked improvement of the meningeal enlargement and disappearance of the nodular lesions.
See this image and copyright information in PMC

References

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